Wyniki wyszukiwania dla: Dravet syndrome - MOST Wiedzy

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Wyniki wyszukiwania dla: Dravet syndrome

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Wyniki wyszukiwania dla: Dravet syndrome

  • Medium voltage drives - challenges and requirements

    Publikacja

    - Rok 2010

    The design and application of medium voltage (MV) drives are associated with different requirements related to the line side and motor side of the drive. This paper presents a brief review of the existing challenges and requirements for employing medium voltage drives in various industries. Line side, motor side, and converterproblems and requirements are described. The aim of the paper is to review the existing problems to allow...

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  • Dis/Trust and data-driven technologies

    Publikacja

    - Internet Policy Review - Rok 2023

    This concept paper contextualises, defines, and systematises the concepts of trust and distrust (and their interrelations), providing a critical review of existing literature so as to identify gaps, disjuncture, and continuities in the use of these concepts across the social sciences and in the context of the consolidation of the digital society. Firstly, the development of the concept of trust is explored by looking at its use...

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  • Use of broad-spectrum antibiotics in children diagnosed with multisystem inflammatory syndrome temporarily associated with SARS-CoV-2 infection in Poland: the MOIS-CoR study

    Publikacja
    • K. Toczyłowski
    • J. Łasecka-Zadrożna
    • I. Pałyga-Bysiecka
    • K. Ludwikowska
    • M. Okarska-Napierała
    • N. Dudek
    • A. Afelt
    • C. Suski
    • M. Kursa
    • T. Jackowska... i 51 innych

    - International Journal of Infectious Diseases - Rok 2022

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  • Mild X-linked Alport syndrome due to the COL4A5 G624D variant originating in the Middle Ages is predominant in Central/East Europe and causes kidney failure in midlife

    Publikacja
    • A. Żurowska
    • O. Bielska
    • P. Daca-Roszak
    • M. Jankowski
    • M. Szczepańska
    • D. Roszkowska-Bjanid
    • E. Kuźma-Mroczkowska
    • M. Pańczyk-Tomaszewska
    • A. Moczulska
    • D. Drożdż... i 18 innych

    - KIDNEY INTERNATIONAL - Rok 2021

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  • MRI assessment of ectopic fat accumulation in pancreas, liver and skeletal muscle in patients with obesity, overweight and normal BMI in correlation with the presence of central obesity and metabolic syndrome

    Publikacja

    - Diabetes Metabolic Syndrome and Obesity-Targets and Therapy - Rok 2019

    Purpose: Obesity, defined as a body mass index (BMI) exceeding 30 kg/m2, is a serious health problem, which can be called an epidemic on a global scale and is one of the most important causes of preventable death. The aim of this study was to assess ectopic fat accumulation in pancreas, liver and skeletal muscle in patients with obesity, overweight and normal BMI in correlation with metabolic syndrome (MetS). Patients and methods:...

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  • Mild X-linked Alport syndrome due to the COL4A5 G624D variant originating in the Middle Ages is predominant in Central/East Europe and causes kidney failure in midlife

    Publikacja
    • A. M. Żurowska
    • O. Bielska
    • P. Daca-Roszak
    • M. Jankowski
    • M. Szczepańska
    • D. Roszkowska-Bjanid
    • E. Kuźma-Mroczkowska
    • M. Pańczyk-Tomaszewska
    • A. Moczulska
    • D. Drożdż... i 18 innych

    - KIDNEY INTERNATIONAL - Rok 2021

    A study of 269 children enrolled into a National Registry for children with persistent glomerular hematuria identified 131 individuals with genetically confirmed X-linked Alport Syndrome. A single variant c.1871G>A p.Gly624Asp (G624D) in COL4A5 was predominant and accounted for 39% of Xlinked Alport Syndrome in unrelated Polish families (44 of 113). To evaluate its origins, the genetic variation in a 2.79 Mb segment encompassing...

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  • Medical transport of ambulances. Analysis of travel time

    Publikacja

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  • Event driven MPC for networked control systems

    Publikacja

    - Rok 2008

    Because of variable delays and stochastic data packets loss networked control systems require suitable algorithms to ensure stability of the control system and guarantee desired control performance. This paper presents the idea of an event driven approach with MPC controller. In opposition to network compensation, where standard regulators are used, the presented solution integrates network with plant. A MPC based controller is...

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  • Excitation-independent constant conductance isfet driver

    Publikacja

    - Metrology and Measurement Systems - Rok 2009

    A new constant conductance driver for ISFETs sensors has been developed. The proposed circuit maintains the sensor operating point at constant drain-source conductance. The combination of a simple, self-balancing resistance bridge and the subtraction half (or similar fraction) of source-drain voltage from the gate-source voltage provides the independence of output signal from current and voltage drivers instability. The use of...

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  • The architecture of distributed systems driven by autonomic patterns

    Publikacja

    - Rok 2006

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  • Worm Gear Drives with Improved Kinematic Accuracy

    Publikacja

    - Materials - Rok 2021

    This paper presents the fundamentals of the design and applications of new worm gear drive solutions, which enable the minimisation of backlash and are characterised by higher kinematic accuracy. Different types of worm surfaces are briefly outlined. Technological problems concerning the principles of achieving a high degree of precision in machining are also described. Special attention is paid to the shaping of conical helical...

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  • Multilevel pharmacokinetics-driven modeling of metabolomics data

    Publikacja

    - METABOLOMICS - Rok 2017

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  • Simulation-Driven Design of Microstrip Antenna Subarrays

    A methodology for computationally efficient simulation-driven design of microstrip antenna subarrays is presented. Our approach takes into account the effect of the feed (e.g., a corporate network) on the subarray side lobe level and allows adjusting both radiation and reflection responses of the structure under design within a single automated process. This process is realized as surrogate-based optimization that produces designs...

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  • Advances in CSI-fed induction motor drives

    Publikacja

    The application of current source inverters (CSI)in induction motor (IM) drives offers a number of advantages,including: voltage boosting capability, natural shoot-throughshort-circuit protection and generation of sinusoidal voltages.The exact generation of sinusoidal voltages is possible thanks tothanks to the effect of the output ac filter capacitors and mayimprove the accuracy of sensorless IM control. The eliminationof high...

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  • Faults and Fault Detection Methods in Electric Drives

    Publikacja

    The chapter presents a review of faults and fault detection methods in electric drives. Typical faults are presented that arises for the induction motor, which is valued in the industry for its robust construction and cost-effective production. Moreover, a summary is presented of detectable faults in conjunction with the required physical information that allow a detection of specific faults. In order to address faults of a complete...

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  • The impact of the temperament model on the behavior of an autonomous driver

    Because it is generally believed that the personality and temperament of a human driver influence his/her behavior on the road, the article presents a computational model of the temperament of an autonomous agent - a driver. First, a short review of the four ideas of Galen’s temperament in psychology is presented. Temperament traits are grouped into four other sets, one of which is chosen for implementation in the project of integration...

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  • Iridium 5d -electron driven superconductivity in ThIr3

    Publikacja

    - PHYSICAL REVIEW B - Rok 2019

    A polycrystalline sample of superconducting ThI r 3 was obtained by arc-melting Th and Ir metals. Powder x-ray diffraction revealed that the compound crystalizes in a rhombohedral crystal structure (R-3m, s.g. #166) with the lattice parameters: a = 5.3394 ( 1 ) Å and c = 26.4228 ( 8 ) Å . Normal and superconducting states were studied by magnetic susceptibility, electrical resistivity, and heat capacity measurements. The results...

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  • Travel Time of Public Transport Vehicles Estimation

    Effective prediction of speed is central to advanced traveler information and transportation management systems. The speed of public transport vehicles is affected by many external factors including traffic volume, organization and infrastructure. The literature presents methods for estimating travel time on sections of a transport network and vehicle arrival at stops, often making use of the AVL (automatic vehicle location). The...

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  • Psychosocial risks associated with the profession of train driver

    Publikacja

    Excellent competencies as well as a good physical and mental health are required in train drivers’ profession. Despite the changes in the structure of employment the train drivers above 46 years and job tenure longer than 30 years are the largest group. The generation gap is becoming more pronounced, and its fulfilment will not be easy. It is related not only to training of new personnel but also promotion of healthy work environment...

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  • Medium-Voltage Drives: Challenges and existing technology

    Publikacja
    • H. Abu-Rub
    • S. Bayhan
    • S. Moinoddin
    • M. Malinowski
    • J. Guziński

    - IEEE Power Eelectronics Magazine - Rok 2016

    The article presents an overview of state-of-art solutions, advances, and design and research trends in medium-voltage (MV) drive technologies - and also discusses the challenges and requirements associated with the use of such drives. The choice and deployment of MV drives in industries are associated with numerous requirements related to the front-end converter (grid side) and inverter (machine side). The focus is on solutions...

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  • Emotions Embodied in the SVC of an Autonomous Driver System

    Publikacja

    A concept of embodied intelligence (EI) is considered. None of such implementations can be fully identified with artificial intelligence. Projects that dare to approach AI and EI should be based on both the AI concepts (symbolic and sub-symbolic), in solving real problems of perception and decision-making. Therefore, the EI, in this paper, is understood as a methodology that uses all available resources and algorithms from the...

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  • Possibility of Fault Detection in Sensorless Electric Drives

    The work presents a fault detection method for an induction motor drive system with inverter output filter. This approach make use of a load torque state observer, which complete structure is presented along with the used control structure. Moreover, the demonstrated drive system operates without rotor speed measurement in conjunction with the multiscalar control. The verification of the demonstrated idea was performed on an experimental...

  • Equivalent standard manoeuvres for pod-driven ships

    Publikacja

    Procedures for carrying out the manoeuvring tests presented in International Maritime Organisation (IMO) resolution MSC.137(76) are based on the capabilities of ships with conventional steering-propulsion systems. Therefore they do not correspond to ships with other steering-propulsion devices, like pod drives. IMO is aware of this shortcoming and for ships with non-conventional steering and propulsion system may permit the use...

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  • eVisa’s impacts on travel and tourism: the case of Turkey.

    Publikacja

    - Journal of Hospitality and Tourism Technology - Rok 2018

    he purpose of this study was to investigate eVisa applications. eVisa is a service that falls under eTourism, whose growing use can be attributed to its ability to simplify the process of obtaining a visa. The objectives of this study were twofold: to explore the eVisa experience of tourists who have previously visited Turkey by using the service and to analyse the perceptions of stakeholders who have contributed to eVisa.

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  • Bioreactors and biophoton-driven biohydrogen production strategies

    Publikacja
    • S. Anjum
    • S. Aslam
    • N. Hussain
    • M. Bilal
    • G. Boczkaj
    • W. Smułek
    • T. Jesionowski
    • H. M. Iqbal

    - INTERNATIONAL JOURNAL OF HYDROGEN ENERGY - Rok 2023

    Given the current issues with global warming and rising greenhouse gas emissions, biohydrogen is a viable alternative fuel option. Technologies to produce biohydrogen include photo fermentation, dark fermentation, direct and indirect bio-photolysis, and two-stage fermentation. Biological hydrogen generation is a green and promising technique with mild reaction conditions and low energy consumption compared to thermochemical and...

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  • Microcontroller driven miniaturized digital depth sounder.

    Przedstawiono schemat blokowy, specyfikację techniczną oraz zasadę działania miniaturowej echosondy cyfrowej, sterowanej mikrokontrolerem PIC16F873.Specjalistyczne oprogramowanie echosondy umożliwia prezentację echogramów w czasie rzeczywistym oraz udostępnianie ich w sieci Internet w typowych przeglądarkach WWW.

  • Experimental evaluation of the PLC-controlled drives properties.

    Publikacja

    - Rok 2003

    Przedstawiono strukturę stanowiska laboratoryjnego do testów oprogramowania PLC do sterowania napędami oraz do prowadzenia eksperymentalnych prób takich napędów. Omówiono zasady prowadzenia testów oprogramowania przed i w trakcie uruchamiania napędu. Przedstawiono przykładowe rezultaty doświadczeń.

  • Potential Benefits Of Electricaly Driven Ferry, Case Study

    Publikacja
    • T. Perić
    • L. Stazić
    • K. Bratić

    - Pedagogika-Pedagogy - Rok 2021

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  • Experimental studies of circuit breaker drives and mechanisms diagnostics

    Publikacja
    • Z. Pochanke
    • W. Chmielak
    • T. Daszczynski

    - Rok 2016

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  • Synthesis of irregular motion mechanisms for production machine drives

    Publikacja
    • T. Martynova
    • V. Skeeba
    • Y. Podgornyj
    • D. Lobanov

    - IOP Conference Series: Materials Science and Engineering - Rok 2020

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  • Knowledge-based performance-driven modeling of antenna structures

    The importance of surrogate modeling techniques in the design of modern antenna systems has been continuously growing over the recent years. This phenomenon is a matter of practical necessity rather than simply a fashion. On the one hand, antenna design procedures rely on full-wave electromagnetic (EM) simulation tools. On the other hand, the computational costs incurred by repetitive EM analyses involved in solving common tasks...

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  • Variable Speed AC Drives with Inverter Output Filters

    Publikacja

    - Rok 2015

    The advance of variable speed drives systems (VSDs) engineering highlights the need of specific technical guidance provision by electrical machines and drives manufacturers, so that such applications can be properly designed to present advantages in terms of both energy efficiency and expenditure. This book presents problems and solutions related to inverter-fed electrical motors. Practically orientated, the book describes the...

  • Autonomous Driver Based on an Intelligent System of Decision-Making

    Publikacja

    The paper presents and discusses a system (xDriver) which uses an Intelligent System of Decision-making (ISD) for the task of car driving. The principal subject is the implementation, simulation and testing of the ISD system described earlier in our publications for the task of autonomous driving. The design of the whole ISD system is a result of a thorough modelling of human psychology based on an extensive literature study. Concepts...

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  • Design and implementation of the driver system for Hamamatsu C12880MA microspectrometer

    Recent miniaturization developments in devices for spectroscopy have reduced greatly their costs and increased their availability for a wide range of users and applications. This paper presents the design and implementation of a driver system for a Hamamatsu C12880MA microspectrometer. The system implementation was carried out and compared using two independent microcontroller modules: Arduino Uno and STM32F411RE Nucleo. We assessed...

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  • High Performance Control of AC Drives with Matlab/ Simulink

    Publikacja

    - Rok 2021

    Explore this indispensable update to a popular graduate text on electric drive techniques and the latest converters used in industry. The Second Edition of High Performance Control of AC Drives with Matlab®/Simulink delivers an updated and thorough overview of topics central to the understanding of AC motor drive systems. The book includes new material on medium voltage drives, covering state-of-the-art technologies and challenges...

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  • Performance‐driven modeling of compact couplers in restricted domains

    Fast surrogate models can play an important role in reducing the cost of EM-driven design closure of miniaturized microwave components. Unfortunately, construction of such models is challenging due to curse of dimensionality and wide range of geometry parameters that need to be included in order to make it practically useful. In this letter, a novel approach to design-oriented modeling of compact couplers is presented. Our method...

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  • Gate Driver with Overcurrent Protection Circuit for GaN Transistors

    The improvement of the gate driver for GaN transistor is presented in this paper. The proposed topology contains the overcurrent protectionwith the two-stage turning off and independent control of turn on and off time of the GaN transistor. The operation of driver and its application in thehalf-bridge converter are described using both simulation and prototype measurements. The overcurrent protection was tested in Double Pulse...

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  • Hybridization-driven gap inU3Bi4Ni3: AB209iNMR/NQR study

    Publikacja
    • S. Baek
    • N. Curro
    • T. Klimczuk
    • H. Sakai
    • E. Bauer
    • F. Ronning
    • J. Thompson
    • T. Klimczuk

    - PHYSICAL REVIEW B - Rok 2009

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  • Driver Fatigue and Road Safety on Poland's National Roads

    This paper presents an overview of factors causing driver fatigue as described in the literature. Next, a traffic crash database for 2003–2007 is used to identify the causes, circumstances and consequences of accidents caused by driver fatigue on Poland’s national roads. The results of the study were used to build a model showing the relationship between the concentration of road accidents and casualties, and the time of day. Finally,...

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  • Semantic Driven Table Understanding in Born-Digital Documents

    Publikacja

    - Rok 2014

    This paper presents a new approach to table understanding, suitable for born-digital PDF documents. Advance beyond the current state of the art in table understanding is provided by the proposed reverse MVC method, which takes advantage of only partial logic structure loss (degradation) in born-digital PDF documents, as opposed to unrecoverable loss (deterioration) taking place in scan based PDF documents.

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  • Risk-driven Software Process Improvement - a Case Study.

    Publikacja

    - Rok 2004

    Artykuł przedstawia studium przypadku praktycznego zastosowania metody sterowanej ryzykiem poprawy procesów programowych w rzeczywistym projekcie informatycznym. Metoda zakłada jawne modelowanie procesu i jego braków (czynników ryzyka), a także wspiera ewolucję procesów. Ponadto zawiera dedykowane techniki identyfikacji ryzyka procesów oraz wywodzenia z niego sugestii poprawy procesów. Techniki te są wbudowane w cykliczną procedurę...

  • IPMSM Control for Electric Vehicle with Separate Wheel Drives.

    Publikacja

    - Rok 2004

    Przedstawiono propozycję hierarchicznej struktury rozproszonej sterowania pojazdu z niezależnym elektrycznym napędem kół. Zaproponowano algorytmy sterowania silnikiem synchronicznym z magnesami trwałymi. Przedstawiono strukturę stanowiska badawczego oraz wstępne wyniki badań symulacyjnych i laboratoryjnych układu.

  • Implementation of the requirements driven quality method in a small IT company

    Publikacja

    - Rok 2005

    Praca przedstawia proces i rezulaty wdrożenia metody RDQC - sterowanej wymaganiami kontroli jakości w rzeczywistej, niedużej firmie informatycznej. Pokazano specyfike firmy i wybranych projektów, omówiono podstawy metody RDQC, plan jej wdrożenia oraz najważniejsze osiągnięte rezultaty.

  • Performance-Driven Surrogate Modeling of High-Frequency Structures

    Publikacja

    The development of modern high-frequency structures, including microwave and antenna components, heavily relies on full-wave electromagnetic (EM) simulation models. Notwithstanding, EM-driven design entails considerable computational expenses. This is especially troublesome when solving tasks that require massive EM analyzes, parametric optimization and uncertainty quantification be-ing representative examples. The employment of...

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  • On the interspike-intervals of periodically-driven integrate-and-fire models

    We analyze properties of the firing map, which iterations give information about consecutive spikes, for periodically driven linear integrate-and-fire models. By considering locally integrable (thus in general not continuous) input functions, we generalize some results of other authors. In particular, we prove theorems concerning continuous dependence of the firing map on the input in suitable function spaces. Using mathematical...

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  • Electric Field-Driven Assembly of Sulfonated Polystyrene Microspheres

    Publikacja
    • A. Mikkelsen
    • J. Wojciechowski
    • M. Rajnak
    • J. Kurimský
    • K. Khobaib
    • A. Kertmen
    • Z. Rozynek

    - Materials - Rok 2017

    A designed assembly of particles at liquid interfaces offers many advantages for development of materials, and can be performed by various means. Electric fields provide a flexible method for structuring particles on drops, utilizing electrohydrodynamic circulation flows, and dielectrophoretic and electrophoretic interactions. In addition to the properties of the applied electric field, the manipulation of particles often depends...

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  • TIME-AND-SPACE STRUCTURE OF FORCE-DRIVEN RIGID SPHEREWAVEFIELD

    Publikacja

    - Rok 2015

    This paper introduces a time-domain, causality-inspired description of a vector-source acoustic wavefield of arbitrary time evolution, where a sphere is a practical realisation of quasi-point contact surface without which a point force would not be able to exert an impact onto non-viscous fluid. At every space location, the resulting acoustic field is described by a pair of physical variables characterising the time evolution of...

  • Size Reduction of Microwave Couplers by EM-Driven Optimization

    Publikacja

    - Rok 2015

    This work addresses simulation-driven design optimization of compact microwave couplers that explicitly aims at circuit footprint area reduction. The penalty function approach allows us to minimize the area of the circuit while ensuring a proper power division between the output ports and providing a sufficient bandwidth with respect to return loss and isolation around the operating frequency. Computational cost of the optimization...

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  • Technology-Driven Internationalization: Central-Eastern European Perspective

    Publikacja

    - Rok 2017

    Since the 1990s of the twentieth century onward, Central-Eastern European countries have been extensively involved in these two processes—regarding increasing share of ICT and high-tech exports in country’s total export value—and additionally, across these economies, changes in the level of access to and use of ICT have been observed. The main target of this research is to contribute to the present state of the art, by proving...

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  • Information-driven network resilience: Research challenges and perspectives

    Publikacja
    • J. Rak
    • D. Papadimitriou
    • H. Niedermayer
    • P. Romero

    - Optical Switching and Networking - Rok 2017

    Internet designed over 40 years ago was originally focused on host-to-host message delivery in a best-effort manner. However, introduction of new applications over the years have brought about new requirements related with throughput, scalability, mobility, security, connectivity, and availability among others. Additionally, convergence of telecommunications, media, and information technology was responsible for transformation...

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